Cystic Fibrosis

Cystic Fibrosis is an inherited lung disease that causes thick secretions to form in the lungs and digestive system that leads to recurrent infections and potential problems with growth.

Our division is accredited by the National Cystic Fibrosis Foundation; we have recently been accredited as a Cystic Fibrosis CORE Center and are no longer an affiliate to Duke University Medical Center. Our division provides multidisciplinary care for the child and family.

Cystic Fibrosis Center

The Division of Pediatric Pulmonology strives to allow children and their families to receive the recommended medical care and education needed to manage their healthcare needs.

Patient-Centered Care

  • We provide a multidisciplinary team to provide care for patients and their families
  • We provide educational programs for health professionals
  • We provide educational programs for families and the community
  • We participate in research to improve outcomes for those affected by Cystic Fibrosis
  • We provide education to the patient and family as the child begins transition into adulthood, in the early teens, so as to have them adequately prepared and psychologically ready to transition to adult providers. 

Multi-faceted Clinical Services

Our clinical services cover a broad range to include evaluation and diagnosis, as well as treatment with focuses on...

  • The promotion of normal growth and development
  • The maintenance of lung health by slowing the progression of Cystic Fibrosis
  • Education to prevent complications and treatment of complications should they arise
  • Support of our patients and families as they adjust their lives to embrace all aspects of CF disease
  • Education of the family and our surrounding community to promote a positive experience for our patients in all aspects of their daily living

Multidisciplinary Care

The Cystic Fibrosis Center of the Children's Hospital of the Greenville Health System has multiple subspecialists who work together to provide multidisciplinary care for pediatric Cystic Fibrosis patients. This interdisciplinary team is the heart of our center and meets to evaluate the clinical, educational and psychosocial needs of our families and their children.

Our primary team consists of pediatric pulmonologists, advanced practice nurses, respiratory therapists, dieticians, social workers and child life therapists. Additional expertise from pediatric gastroenterologists, endocrinologists, infectious disease specialists, genetic counselors, pharmacologists, and physical therapists are available.

Meet Your Clinic Team

Dr. Steve Snodgrass
Director Cystic Fibrosis Center of Children's Hospital of Greenville Health System
Medical Director of the Division of Pediatric Pulmonology of Children's Hospital of Greenville Health System
Pediatric Pulmonologist

Dr. Michael Fields, PhD
Medical Director of Pediatric Respiratory Care Services
Associate Cystic Fibrosis Center Director
Pediatric Pulmonologist

Dr. Sterling Simpson, MSc in Exercise Physiology
Pediatric Pulmonologist

Lisa A. DuBose, NP
Nurse Practitioner

Rebecca Peace, RRTE, RCP
Cystic Fibrosis Registry Coordinator
Respiratory Therapist

Sherrie Bagwell, CRT, RCP
Respiratory Therapist

Sheena Brown, RRT
Respiratory Therapist

Kristan Stewart, RD
Registered Dietician

Christy Clarke, LMSW
Social Worker

Mitzi Privette, M. Ed., CCLS
Child Life Therapist

Cystic Fibrosis Research

The Cystic Fibrosis Center is currently involved in research that is utilized to evaluate and enhance the treatment of the child with Cystic Fibrosis. We are involved in studies listed below

Cystic Fibrosis Registry

This multi-center, longitudinal follow-up study of patients with cystic fibrosis for monitoring pulmonary function, pulmonary exacerbations, and the safety of long-term treatments as patients are tracked over their lifetime and trends are then able to be identified due to the sheer volume of data that is entered and evaluated.

Sibling Study

We have participated with this research study which has now closed and we are looking forward to participate in more clinical research studies.

Referral for Research

Our center is in close contact with other local centers and the research they are conducting. We refer patients who qualify for studies and are interested in participating and provide those centers with the necessary data needed to enroll patients in research.

Quality Improvement Measures

Our center is constantly working to improve the care of our patients and their families. A variety of quality improvement measures are done yearly to promote constant excellence in the care your child receives. We work very closely with the Cystic Fibrosis Foundation as we continue on our journey of providing excellence in the care of the Cystic Fibrosis patient and their family.

  • Enhancing communication of patient needs and assessments with our CF Team via Team meetings with a goal of 95% full attendance
  • Assessing FEV1 for improvement given recent changes in CF Guidelines and therapies in comparison to our average for 2015
  • Obtaining mental health assessments for those 12 years and older this calendar year with goal of 95% completion 
  • Yearly evaluation by Registered dietitian, social worker, and respiratory therapist with a goal of 95%

Cystic Fibrosis Newborn Screening

Children with Cystic Fibrosis benefit from early intervention. The earlier a child is diagnosed and cared for by a Cystic Fibrosis Center, the better the child's outcomes are. Cystic Fibrosis is a genetic disease that is caused by a 'recessive' gene. Recessive means that the child must receive two copies of the gene, one from each parent, for the gene to cause disease.

A Cystic Fibrosis carrier is a person with one working copy of the CF gene. Typically a carrier is healthy and does not have signs of CF.

When EACH parent has a WORKING copy of a CF gene and are carriers, then EACH pregnancy...

  • There is a 25% chance of having a child with Cystic Fibrosis
  • There is a 25% chance of having a child without Cystic Fibrosis or carrier status
  • There is a 50% chance of having a child that is a carrier

These percentages are the SAME for EVERY pregnancy, even if the couple has already had a child with CF.

Immunoreactive Trypsinogen (IRT)

The IRT is the newborn screen that detects how much IRT is in the baby's blood. It is a digestive enzyme made by the pancreas. Infants with CF will often have an elevated IRT that remains so for several months after birth. This test is done in the hospital prior to the newborn being released as part of the South Carolina Newborn Screening Program. If the test is high, it is repeated by the PCP and a sweat chloride is typically ordered, and often a referral to our center is made. Remember though, that only about 1 in 10 babies with a high IRT actually have Cystic Fibrosis. See www.cff.org for more information.

Sweat Chloride Test

The sweat test is the gold standard for diagnosing Cystic Fibrosis. The sweat test measures how much chloride, or salt, is in your baby's sweat. The CF gene affects how the chloride will move thru your baby's cells. The sweat test does not hurt and results are available on the same day.